Repository logo
 
Publication

Domiciliary High-Flow Nasal Therapy in Primary Ciliary Dyskinesia

2023-01Journal article Open access
Simple item page
dc.contributor.authorGomes, Rita
dc.contributor.authorQueirós, Joana
dc.contributor.authorBorges, Joana
dc.contributor.authorCardoso, Ana Lúcia
dc.contributor.authorBarbosa, Telma
dc.date.accessioned2024-06-18T10:06:20Z
dc.date.available2024-06-18T10:06:20Z
dc.date.issued2023-01
dc.description.abstractWe report the case of an adolescent with severe primary ciliary dyskinesia (PCD) phenotype associated with a rare genotype. His clinical condition deteriorated, with daily cough and breathlessness, hypoxemia, and lung function decline. Despite being started on home noninvasive ventilation (NIV), the symptoms progressed to dyspnea at rest and thoracic pain. High-flow nasal cannula (HFNC) was started during the daytime as an adjuvant to NIV, and he was started on regular oral opioids for pain and dyspnea control. There was a clear improvement in comfort and dyspnea and breathing work relief. Additionally, better exercise tolerance was also noted. He is currently on the lung transplant waiting list. We aim to emphasize the benefits of HFNC as an add-on therapy for the management of chronic breathlessness since our patient experienced an improvement in breathing and exercise tolerance. However, there is a paucity of studies regarding domiciliary HFNC, particularly in pediatric age. Therefore, further studies are needed to achieve optimal and personalized care. Close monitoring and frequent reassessment in a specialized center are key to adequate management.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationGomes R, Queirós J, Borges J, Cardoso AL, Barbosa T. Domiciliary High-Flow Nasal Therapy in Primary Ciliary Dyskinesia. Cureus. 2023;15(1):e34177. doi:10.7759/cureus.34177pt_PT
dc.identifier.doi10.7759/cureus.34177pt_PT
dc.identifier.issn2168-8184
dc.identifier.urihttp://hdl.handle.net/10400.16/2954
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherCureus, Inc.pt_PT
dc.relation.publisherversionhttps://www.cureus.com/articles/133082-domiciliary-high-flow-nasal-therapy-in-primary-ciliary-dyskinesia#!/pt_PT
dc.rights.urihttp://creativecommons.org/licenses/by/4.0/pt_PT
dc.subjecthigh-flow nasal oxygenpt_PT
dc.subjectnoninvasive mechanical ventilationpt_PT
dc.subjectpalliative carept_PT
dc.subjectprimary ciliary dyskinesia (pcd)pt_PT
dc.subjectrespiratory insufficiencypt_PT
dc.titleDomiciliary High-Flow Nasal Therapy in Primary Ciliary Dyskinesiapt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.conferencePlaceUnited States of Americapt_PT
oaire.citation.issue1pt_PT
oaire.citation.startPagee34177pt_PT
oaire.citation.titleCureuspt_PT
oaire.citation.volume15pt_PT
person.familyNameBarbosa
person.givenNameTelma
person.identifier.ciencia-idD314-0057-1A9B
person.identifier.orcid0000-0003-4641-2898
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT
relation.isAuthorOfPublication57600d9a-7be8-42a3-b550-24a1156963fa
relation.isAuthorOfPublication.latestForDiscovery57600d9a-7be8-42a3-b550-24a1156963fa

Files

Original bundle
Now showing 1 - 1 of 1
Thumbnail Image
Name:
Gomes-2023-Domiciliary-high-flow-nasal-therapy.pdf
Size:
232.58 KB
Format:
Adobe Portable Document Format
Download
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.44 KB
Format:
Item-specific license agreed upon to submission
Description:
Download

Collections

SPM - Artigos publicados em revistas indexadas na Pubmed/Medline