Repository logo
 
Publication

Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis

2020-04-30Journal article Open access
Simple item page
dc.contributor.authorPinheiro, Maria Guiomar
dc.contributor.authorAlves, Ana Margarida
dc.contributor.authorNeves, Isabel
dc.contributor.authorSequeira, Teresa
dc.date.accessioned2021-11-22T15:23:17Z
dc.date.available2021-11-22T15:23:17Z
dc.date.issued2020-04-30
dc.description.abstractPulmonary hypoplasia or agenesis is a rare congenital disorder that results in lung underdevelopment. This disease is usually found in children but rarely encountered in adults. We describe the case of an 84-year-old woman diagnosed with a unilateral pulmonary hypoplasia presenting simultaneously with left pulmonary artery hypoplasia. Due to this condition, the patient had a lifelong history of pulmonary infections that resulted in several bronchiectases in the affected lung. Moreover, the pulmonary artery hypoplasia led to the development of pulmonary hypertension and collateral circulation causing hemoptysis, giving rise to the patient attending the emergency department. Although we were able to medically manage the hemoptysis, it can be fatal and require surgical intervention. Hence, an early diagnosis is essential so that appropriate follow-up and prompt prevention and treatment of complications, such as pulmonary infections, hemoptysis and pulmonary hypertension, are achieved. Learning points: Although rare and typically associated with childhood, lung and pulmonary artery hypoplasia can in exceptional cases be present in adult life.The diagnosis of lung and pulmonary artery hypoplasia is challenging in adults as they can easily be mistaken for more common diseases.Symptoms and complications may be life-threatening, including dyspnea, hemoptysis, recurrent pulmonary infections and pulmonary hypertension.An early diagnosis is extremely important because it allows a close follow-up with consequent timely detection and treatment of serious complications, especially pulmonary hypertension.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationPinheiro G, Alves AM, Rodrigues Neves I, Sequeira T. Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis. Eur J Case Rep Intern Med. 2020;7(7):001490. doi:10.12890/2020_001490pt_PT
dc.identifier.doi10.12890/2020_001490pt_PT
dc.identifier.issn2284-2594
dc.identifier.urihttp://hdl.handle.net/10400.16/2599
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherSMC Mediapt_PT
dc.relation.publisherversionhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC7350963/pt_PT
dc.rights.urihttp://creativecommons.org/licenses/by/4.0/pt_PT
dc.subjectRadiologypt_PT
dc.subjectcongenital disorderspt_PT
dc.subjecthemoptysispt_PT
dc.subjectlung hypoplasiapt_PT
dc.subjectpulmonary artery agenesispt_PT
dc.subjectpulmonary artery hypoplasiapt_PT
dc.subjectrespiratory medicinept_PT
dc.titleLeft Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysispt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.conferencePlaceItalypt_PT
oaire.citation.issue7pt_PT
oaire.citation.titleEuropean Journal of Case Reports in Internal Medicinept_PT
oaire.citation.volume7pt_PT
person.familyNamePinheiro
person.familyNameda Cruz Alves
person.givenNameMaria Guiomar
person.givenNameAna Margarida
person.identifier.ciencia-idAD18-3B56-DD7E
person.identifier.orcid0000-0003-1497-1054
person.identifier.orcid0000-0003-1598-6282
person.identifier.scopus-author-id57194153375
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT
relation.isAuthorOfPublicationae5810a4-751a-42d0-802f-1bb0e17e0032
relation.isAuthorOfPublicationecc89742-cc1d-4ea1-a815-97ad62e39ff1
relation.isAuthorOfPublication.latestForDiscoveryecc89742-cc1d-4ea1-a815-97ad62e39ff1

Files

Original bundle
Now showing 1 - 1 of 1
Thumbnail Image
Name:
2020-Left-lung-and-pulmonary-artery-hypo.pdf
Size:
814.49 KB
Format:
Adobe Portable Document Format
Download

Collections

MED 1A - Artigos publicados em revistas indexadas na Pubmed/Medline
SRD - Artigos publicados em revistas indexadas na Medline