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Syndrome in question

dc.contributor.authorRosmaninho, A.
dc.contributor.authorCarvalho, S.
dc.contributor.authorOujo, E.
dc.contributor.authorHorta, M.
dc.date.accessioned2017-04-24T14:12:21Z
dc.date.available2017-04-24T14:12:21Z
dc.date.issued2016-04
dc.description.abstractNeurofibromatosis is extremely variable in its presentation. Segmental neurofibromatosis (SNF), which corresponds to NF-type 5 in the Riccardi classification, is a rare disorder. It may go unrecognized if few lesions are observed. We present a case of segmental neurofibromatosis in a 28 year-old patient who presented with multiple papules and nodules distributed in dermatomal fashion on the trunk. The histopathological examination of the lesions revealed a non-encapsulated, well-circumscribed spindle cell neoplasm, which was consistent with neurofibromas.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationAn Bras Dermatol. 2016 Apr;91(2):245-7.pt_PT
dc.identifier.doi10.1590/abd1806-4841.20164231pt_PT
dc.identifier.issn0365-0596
dc.identifier.issn1806-4841
dc.identifier.urihttp://hdl.handle.net/10400.16/2074
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherSociedade Brasileira de Dermatologiapt_PT
dc.relation.publisherversionhttp://www.scielo.br/pdf/abd/v91n2/0365-0596-abd-91-02-0245.pdfpt_PT
dc.subjectNeurofibromapt_PT
dc.subjectNeurofibromatosispt_PT
dc.subjectsegmentar neurofibromatosispt_PT
dc.titleSyndrome in questionpt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.conferencePlaceBrazilpt_PT
oaire.citation.endPage247pt_PT
oaire.citation.issue2pt_PT
oaire.citation.startPage245pt_PT
oaire.citation.titleAnais Brasileiros de Dermatologiapt_PT
oaire.citation.volume91pt_PT
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT

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