Dionísio, Sílvia RodriguesVentura, Eduardo SimõesFerreira, Ângela TavaresGonçalves, Joana BolinhaSaleiro, Rute VazMarques, Hugo MartinsDias, Alfredo Figueiredo2022-03-212022-03-212020Dionísio SR, Ventura ES, Ferreira ÂT, et al. Mandibular meningioma-a rare case report of a second extracranial meningioma and a systematic literature review. J Surg Case Rep. 2020;2020(8):rjaa257. doi:10.1093/jscr/rjaa2572042-8812http://hdl.handle.net/10400.16/2669Meningiomas are benign tumours common in the central nervous system. Primary extracranial meningiomas in the jaws are extremely rare. We performed a systematic review of all the primary extracranial meningioma arising in the jawbones reported in the English-language literature including indexed and non-indexed journals and we report a unique case in our hospital of a man with two primary extracranial meningiomas, the first frontal intradiploic and 16 years later, a second located in the mandible. We found 14 cases with primary jaws meningioma and we report another one. A mandibular predominance was observed with only four cases in the maxilla. Most of them occurred in women, with a mean age of 35.9 years. It is the first published case of a patient with two primary extracranial meningiomas one of them in the mandible, which the gender, age and laterality of the lesion are less frequent.engjournal article10.1093/jscr/rjaa257