Rosmaninho, A.Carvalho, S.Oujo, E.Horta, M.2017-04-242017-04-242016-04An Bras Dermatol. 2016 Apr;91(2):245-7.0365-05961806-4841http://hdl.handle.net/10400.16/2074Neurofibromatosis is extremely variable in its presentation. Segmental neurofibromatosis (SNF), which corresponds to NF-type 5 in the Riccardi classification, is a rare disorder. It may go unrecognized if few lesions are observed. We present a case of segmental neurofibromatosis in a 28 year-old patient who presented with multiple papules and nodules distributed in dermatomal fashion on the trunk. The histopathological examination of the lesions revealed a non-encapsulated, well-circumscribed spindle cell neoplasm, which was consistent with neurofibromas.engNeurofibromaNeurofibromatosissegmentar neurofibromatosisjournal article10.1590/abd1806-4841.20164231