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Successful pregnancy in a severely hypoxemic patient with pulmonary alveolar proteinosis

2011Journal article Open access
http://hdl.handle.net/10400.16/869
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Authors

Belchior, I.
Cerdeira, A.
Santos, M.
Braga, J.
Aragâo, I.
Martins, A.

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Abstract(s)

Abstract Pulmonary alveolar proteinosis (PAP) is a rare disorder characterized by abnormal accumulation of a lipoproteinaceous material in the alveoli, which may lead to respiratory failure and has an associated high risk for infections. The mainstay treatment for PAP is whole lung lavage. A pregnant woman, previously diagnosed with primary PAP, the most common form of PAP, was admitted with dyspnea and worsening respiratory function. In one month period, a wholelung bronchopulmonary lavage was performed twice, with clinical and functional improvement. Pregnancy was carried to term and a healthy baby was delivered. The mechanisms of respiratory impairment are discussed as well as treatment options and response. Resumo A proteinose alveolar pulmonar (PAP) é uma doença rara caracterizada pela acumulação anormal de material lipoproteináceo nos alvéolos, que pode levar a insufi ciência respiratória, estando associada a um risco elevado de infecções. O tratamento gold-standard da PAP é a lavagem pulmonar total.

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Keywords

Pregnancy Pulmonary alveolar proteinosis Pulmonary lavage Respiratory failure Gravidez Proteinose alveolar Pulmonar Lavagem pulmonar Insuficiência respiratória

URI

http://hdl.handle.net/10400.16/869

Citation

Rev Port Pneumol. 2011 May-Jun;17(3):139-42

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Revista portuguesa de pneumologia

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