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Successful pregnancy in a severely hypoxemic patient with pulmonary alveolar proteinosis

dc.contributor.authorBelchior, I.
dc.contributor.authorCerdeira, A.
dc.contributor.authorSantos, M.
dc.contributor.authorBraga, J.
dc.contributor.authorAragâo, I.
dc.contributor.authorMartins, A.
dc.date.accessioned2011-11-20T05:17:23Z
dc.date.available2011-11-20T05:17:23Z
dc.date.issued2011
dc.description.abstractAbstract Pulmonary alveolar proteinosis (PAP) is a rare disorder characterized by abnormal accumulation of a lipoproteinaceous material in the alveoli, which may lead to respiratory failure and has an associated high risk for infections. The mainstay treatment for PAP is whole lung lavage. A pregnant woman, previously diagnosed with primary PAP, the most common form of PAP, was admitted with dyspnea and worsening respiratory function. In one month period, a wholelung bronchopulmonary lavage was performed twice, with clinical and functional improvement. Pregnancy was carried to term and a healthy baby was delivered. The mechanisms of respiratory impairment are discussed as well as treatment options and response. Resumo A proteinose alveolar pulmonar (PAP) é uma doença rara caracterizada pela acumulação anormal de material lipoproteináceo nos alvéolos, que pode levar a insufi ciência respiratória, estando associada a um risco elevado de infecções. O tratamento gold-standard da PAP é a lavagem pulmonar total.por
dc.identifier.citationRev Port Pneumol. 2011 May-Jun;17(3):139-42por
dc.identifier.issn0873-2159
dc.identifier.urihttp://hdl.handle.net/10400.16/869
dc.language.isoengpor
dc.peerreviewedyespor
dc.publisherRevista portuguesa de pneumologiapor
dc.relation.publisherversionhttp://apps.elsevier.es/watermark/ctl_servlet?_f=10&pident_articulo=90020264&pident_usuario=0&pcontactid=&pident_revista=420&ty=50&accion=L&origen=elsevier&web=www.elsevier.es&lan=en&fichero=320v17n03a90020264pdf001_2.pdfpor
dc.subjectPregnancypor
dc.subjectPulmonary alveolar proteinosispor
dc.subjectPulmonary lavagepor
dc.subjectRespiratory failurepor
dc.subjectGravidezpor
dc.subjectProteinose alveolar Pulmonarpor
dc.subjectLavagem pulmonarpor
dc.subjectInsuficiência respiratóriapor
dc.titleSuccessful pregnancy in a severely hypoxemic patient with pulmonary alveolar proteinosispor
dc.title.alternativeGravidez de termo em doente com proteinose alveolar e insufi ciência respiratória gravepor
dc.typejournal article
dspace.entity.typePublication
oaire.citation.conferencePlaceLisboapor
oaire.citation.endPage142por
oaire.citation.issue17(3)por
oaire.citation.startPage139por
oaire.citation.titleRevista Portuguesa de Pneumologiapor
rcaap.rightsopenAccesspor
rcaap.typearticlepor

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